Abstract. Background: Hypertrophic pachymeningitis is an uncommon disorder that causes a localized or diffuse thickening of the dura mater and has been. Summary: Idiopathic hypertrophic cranial pachymeningitis is a rare inflammatory disease with diffused involvement of the dura. Often, the definite diagnosis is. Hypertrophic pachymeningitis is a unique clinical entity characterised by fibrosis and thickening of the duramater with resulting neurological dysfunction.

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Log in Sign up. Hypertrophic pachymeningitis is a rare disorder of diverse etiology.

Articles Cases Courses Quiz. A case of chronic hypertrophic cranial pachymeningitis causing cranial polyneuropathy and unilateral central retinal vein occlusion. Cerebrospinal fluid analysis revealed normal cell count, protein and sugar levels.

Non-enhanced CT scans show thickened, hyperdense dura, typically pachymenngitis the tentorium, tentorial ridge, falx, and prepontine brain stem with marked enhancement on contrast administration.

Varied manifestations of a single disease entity. Articles Current Issue Ahead of print Archive. The cell infiltration was marked at the surface of the dura mater.

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Hypertrophic pachymeningitis

Imaging appearance of pachymeningeal tuberculosis. Arch Neurol Psychiatry; Combined therapy of corticosteroid and azathioprine in hypertrophic cranial pachymeningitis. Hypertrophic cranial pachymeningitis involving the pituitary gland: Neurol Med Chir ; Neuroimaging studies revealed diffuse or localized thickening of the dura, and MRI findings were key to diagnosis of this disorder.

Hypertrophic pachymeningitis can be diagnosed with contrast MRI of brain when the clinician maintains pachymeningitiis high index of suspicion for this condition. Published by Wolters Kluwer – Medknow. Hyperrtrophic quiz yourself on this article, log in to see multiple choice questions.

Hypertrophic pachymeningitis

It was first described by Charcot and later by Naffziger and Stern. MR imaging revealed diffuse hypertdophic enhancement and thickening, along with left fronto parieto occipital edema.

A case of rheumatoid pachymeningitis. Herein are described 14 patients with idiopathic hypertrophic pachymeningitis; their clinical, laboratory and radiological findings, as well as their treatment, are analyzed. All patients were treated with corticosteroid and improved intially, but half of them experienced relapses.

Many patients had mild pachymeninggitis moderate elevation of C-reactive protein, and three patients had perinuclear antineutrophil cytoplasmic antibody. Rinsho Shinkeigaku ; Report of a case and review of literature. It can involve the cranial or the spinal dura or both. No Shinkei Geka ; On clinical examination, she had no perception of light in pachymenongitis the eyes and ophthalmoscopic examination showed pachymeningtis of cup with slightly hyperemic fundi.


Magnetic resonance imaging MRI of the brain showed diffuse enhancement with thickening of the meninges. Gadolinium-enhanced T1-weighted MR images show marked enhancement of the dural edges. Multiple meningiomas Multiple meningiomas. Fungal and AFB culture were negative.

Open access journal indexed with Index Medicus. Idiopathic hypertrophic pachymeningitis is a rare disorder of unknown origin. Loading Stack – 0 images remaining.

There were no giant cells, caseation necrosis, or epitheloid granuloma. Hypertrophic cranial pachymeningitis involving dural sinuses: